| Henoch-Schonlein Purpura | Small | – | Purpura (non-blanching rash) on extensor surfaces IgA nephritis Abdominal pain, arthritis, haematuria |
| Microscopic Polyangiitis | Small | p-ANCA | Glomerulonephritis Diffuse alveolar haemorrhage |
| Granulomatosis with Polyangiitis | Small | c-ANCA | Nasal symptoms Respiratory symptoms Glomerulonephritis |
| Eosinophilic Granulomatosis with Polyangiitis | Small | p-ANCA Raised eosinophils | Late-onset asthma Rhinosinusitis and rhinitis |
| Polyarteritis Nodosa | Medium | – | Renal impairment Essential hypertension Cardiovascular events Tender skin nodules |
| Kawasaki disease | Medium | – | High fever (more than 5 days) Widespread rash Bilateral Conjunctivitis Strawberry tongue Coronary artery aneurysms |
| Giant cell arteritis | Large | Raised ESR | Unilateral headache Scalp tenderness Vision loss |
| Takayasu’s Arteritis | Large | – | Aortic arch affected “Pulseless” disease |